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Complete atrioventricular block as the first manifestation of dermatomyositis

https://doi.org/10.18087/cardio.2022.10.n2181

Abstract

Dermatomyositis is a rare systemic autoimmune disease characterized by primary damage of the skin and striated muscles with the development of chronic muscle weakness. Due to the polymorphic nature of the clinical picture, early diagnosis of dermatomyositis is challenging since patients may visit different specialists depending on predominating symptoms. This entails a late diagnosis and, as a result, the absence of necessary treatment. The article presents a clinical case of a late diagnosis of dermatomyositis, which resulted in the development of autoimmune myocarditis with complete atrioventricular block in a female patient.

About the Authors

D. A. Vorobeva
Research Institute of Cardiology, Tomsk National Research Medical Center of the Russian Academy of Sciences
Russian Federation

 Junior Research Scientist, Department of Emergency Cardiology, Cardiology Research Institute, Tomsk National Research Medical Center, Russian Academy of Sciences

Tomsk, Russia



Z. O. Dasheeva
Siberian State Medical University
Russian Federation

1nd-Year Medical Resident, Department of Cardiology, Siberian State Medical University

Tomsk, Russia



V. V. Ryabov
Research Institute of Cardiology, Tomsk National Research Medical Center of the Russian Academy of Sciences; Siberian State Medical University
Russian Federation

Dr. Sci. (Med.), Associate Professor, Head of the Department of Emergency Cardiology, Deputy Director for Scientific and Therapeutic Work, Cardiology Research Institute, Tomsk National Research Medical Center, Russian Academy of Sciences; Head of the Department of Cardiology, Siberian State Medical University

Tomsk, Russia



S. V. Popov
Research Institute of Cardiology, Tomsk National Research Medical Center of the Russian Academy of Sciences
Russian Federation

Dr. Sci. (Med.), Professor, Full Member of the Russian Academy of Sciences, Head of the Department of Interventional Arrhythmology, Director of Cardiology Research Institute, Tomsk National Research Medical Center, Russian Academy of Sciences

Tomsk, Russia



References

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3. Xiong A, Hu Z, Zhou S, Qiang Y, Song Z, Chen H et al. Cardiovascular events in adult polymyositis and dermatomyositis: a meta-analysis of observational studies. Rheumatology. 2022;61(7):2728–39. DOI: 10.1093/rheumatology/keab851

4. Aggarwal R, Rider LG, Ruperto N, Bayat N, Erman B, Feldman BM et al. 2016 American College of Rheumatology/European League Against Rheumatism criteria for minimal, moderate, and major clinical response in adult dermatomyositis and polymyositis: An International Myositis Assessment and Clinical Studies Group/Paediatric Rheumatology International Trials Organisation Collaborative Initiative. Annals of the Rheumatic Diseases. 2017;76(5):792–801. DOI: 10.1136/annrheumdis-2017-211400

5. Lushpaeva Yu.A., Patrikeeva I.M., Evenko A.Yu., Pavlova N.Yu. Myopathy as a manifestation of paraneoplastic polymyositis. Medical Science And Education Of Ural. 2021;22(3):58–62. DOI: 10.36361/1814-8999-2021-22-3-58-62


Supplementary files

1. Полная атриовентрикулярная блокада как первое проявление дерматомиозита. Дополнительные материалы
Subject
Type Исследовательские инструменты
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For citations:


Vorobeva D.A., Dasheeva Z.O., Ryabov V.V., Popov S.V. Complete atrioventricular block as the first manifestation of dermatomyositis. Kardiologiia. 2022;62(10):74-76. (In Russ.) https://doi.org/10.18087/cardio.2022.10.n2181

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ISSN 0022-9040 (Print)
ISSN 2412-5660 (Online)